A new publication is available in Rare Diseases and Orphan Drugs Journal. The article “Cholelithiasis as a Result of Hereditary Spherocytosis – 5-Year Experience” presents the clinical experience of a pediatric surgery department in the management of children with hereditary spherocytosis and concomitant cholelithiasis.
Hereditary spherocytosis is the most common hemolytic anemia in northern Europe, and cholelithiasis is a frequent complication. The paper summarizes a five-year experience with seven children – three boys and four girls – with a mean age of 9.56 years and moderate or severe hereditary spherocytosis, all of whom underwent open splenectomy. All patients also had cholelithiasis, and four of them underwent synchronous cholecystectomy.
It is reported that the children who did not undergo cholecystectomy had no postoperative biliary complaints. All patients were vaccinated preoperatively against pneumococci, meningococci, and Haemophilus influenzae type B. No postoperative complications were reported.
Read the full article here:
https://journal.raredis.org/index.php/RBLS/article/view/233