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Primary ciliary dyskinesia

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The journal Expert Review of Respiratory Medicine has published an article about Primary ciliary dyskinesia (PCD). It’s a rare heterogeneous disorder, usually inherited as an autosomal recessive condition but X-linked inheritance is also described. Abnormal ciliary function in childhood leads to neonatal respiratory distress in term infants, persistent wet cough, bronchiectasis, chronic rhinosinusitis, and hearing impairment; approximately 50% of patients have situs inversus. The full-text article you can find here.

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